MCMedicalCodingSoftware
I27.0

I27.0: Primary pulmonary hypertension

Billable / specific codeICD-10-CM

I27.0 is a billable, specific ICD-10-CM code for primary pulmonary hypertension. It is valid for submission on a claim.

Check I27.0 with the rest of the claim: free scrubber

Excludes1: never code together

These conditions cannot occur together. Billing both on the same encounter is a denial.

  • persistent pulmonary hypertension of newborn (P29.30)
  • pulmonary hypertension NOS (I27.20)
  • secondary pulmonary arterial hypertension (I27.21)
  • secondary pulmonary hypertension (I27.29)

Inclusion terms

Alternative wordings a physician may use in the chart for this same code.

  • Heritable pulmonary arterial hypertension
  • Idiopathic pulmonary arterial hypertension
  • Primary group 1 pulmonary hypertension
  • Primary pulmonary arterial hypertension

Risk adjustment

I27.0 risk-adjusts. Under the CMS-HCC V28 model it maps to this category:

  • HCC 226 Heart Failure, Except End Stage and Acute0.360 RAF

Coefficient shown for the Community Non-dual Aged segment. A higher HCC in the same hierarchy will suppress this one, so capturing it does not always add score. Look up the whole chart to see which of its HCCs the hierarchy would zero.

Medicare coverage

I27.0 is named in 26 Medicare coverage policies: 26 listing it as supporting medical necessity. Which one applies depends on your Medicare contractor.

  • A52466Nebulizers - Policy Article
  • A52850Billing and Coding: Cardiac Catheterization and Coronary Angiography
  • A56423Billing and Coding: Cardiology Non-emergent Outpatient Stress Testing
  • A56451Billing and Coding: Cardiac Computed Tomography (CCT) and Coronary Computed Tomography Angiography (CCTA)

Alphabetic index entries that lead here

  • Arrillaga-Ayerza syndrome(pulmonary sclerosis with pulmonary hypertension)
  • Ayerza's disease or syndrome(pulmonary artery sclerosis with pulmonary hypertension)
  • Cardiopathia nigra
  • Arteriosclerosis, arteriosclerotic›pulmonary(idiopathic)
  • Disease, diseased›Ayerza's(pulmonary artery sclerosis with pulmonary hypertension)
  • Hypertension, hypertensive›lesser circulation
  • Syndrome›Arrillaga-Ayerza
  • Syndrome›Ayerza(-Arrillaga)
  • Syndrome›cardiacos negros
  • Disease, diseased›heart›black
  • Hypertension, hypertensive›pulmonary›primary(idiopathic)
  • Sclerosis, sclerotic›pulmonary›artery

Code history

Unchanged in every release from FY2024 to FY2027.

Other codes under I27

ICD-10-CMFY2027· effective October 1, 2026

Loaded directly from the CMS/NCHS ICD-10-CM public-domain release: see data sources and our editorial policy. If this page disagrees with the CMS tabular list, this page is wrong. Reference information for professional coders; not medical or billing advice.